A clinical case of amyopathic dermatomyositis
Keywords:
periorbital edema and erythema, primary Idiopathic dermatomyositis, amyopathic dermatomyositisAbstract
We present the case report of a 24-year-old woman with periorbital oedema and erythema. Laboratory findings, which included a skin biopsy, established the diagnosis of dermatomyositis. The aetiology and pathogenesis of this disease remain unknown. Both children and adults can be afflicted with dermatomyositis. To diagnose a Primary Idiopathic Dermatomyositis an associated connective tissue disorder or a malignancy must be excluded. Dermatomyositis not uncommonly presents solely with cutaneous manifestations. The recently proposed concept of amyopathic dermatomyositis has been the source of much controversy. ln reference to this case some considerations regarding clinicai features, treatment and prognosis are made.
Downloads
References
Bradley Walter G. Tandan Rup. Dermatomyositis and Polymyositis. ln Harrison 's et al. Principles of Internal Medicine.New York. McGraw-Hill. 1991: 2108-2111.
Wartmann Robert L. Miopatias inllamatórias idiopáticas. ln: Bennet, J. Claude . Plum Fred et al. Cecil Tratado de Medicina Interna. Rio de Janeiro. Guanabara Koogan. 1997: 1658-1662.
Hughes GRY. Connective Tissue Diseases. Cambridge, Backwell Scientific Publications 1994:13
Miller FW. Humoral immunity and imunogenetics in the idiopatic inflammatory myopaties. Curr Opin Rheum 1991: 3: 901-910
Kalnvidouris AE. lmmune aspects of myositis. Curr Opin Rheum 1992: 4: 809-814.
Serralrice. G. Dermatopolymyosites. ln: Marcel - Francis Kahn e colaboradores, Les Maladies_Systémiques 1991: 473-492.
Fung WK. Chan HL. Lam WM. Amyopathic dermatomyositis in Hong Kong - association with nasopharyngeal carcinoma. lnt J Dermatol 1998: 37 (9): 659-663.
McKce H. Phillip. Pathology of the Skin. London. Mosby - Wolkfe1996 1133-1137.
Ng YT, Ouvrier RA, Wu T. Drug Therapy in juvenile dermatomyositis: follow-up Study. J Child Neurol 1998: 13 (3): 109-112.
Rider LG, Miller FW. Classitieation and treatmcnt of the juvenil idiopathic inflammatory myopathies. Rhcum. Dis. Clin. North Am 1997 :23 (3): 619-655.
1. Morgan SH. Bernstein RM, Hughes GRY. lntractable polymyositis: prolonged remission induced by total body irradiation. J Royal Soc of Med 1985: 78: 496-497
Silva, Pereira JA. Clínica do Lupus Eritematoso Sistémico e das outras doenças difusas do tecido conjuntivo. Cadernos de Reumatologia 1992; 3:95-104.
Collison CH, Sinal SH, Jorizzo JL, Walker FO, Monu JU, Snyder J. Juvenile dermatomyositis and polymyositis: a follow-up study of long-term sequelae. South Med J 1998:( 1):17-22.
Tanimoto et al. Classification Criteria for Polymyositis and Dermatomyositis. J Rheumatol 1995: 22 : 668-674.
Additional Files
Published
How to Cite
Issue
Section
License
This work is licensed under a Creative Commons Attribution 4.0 International License.
Copyright (c) 2023 Medicina Interna
Open Access
