Progressive systemic sclerosis - An unusual presentation

Authors

  • Ana Ribeiro da Cunha Assistente Hospitalar Eventual de Medicina Interna, Serviço 1 de Medicina do Hospital de Santo António dos Capuchos, Lisboa
  • José Lourenço Assistente Hospitalar Eventual de Medicina Interna, Serviço 1 de Medicina do Hospital de Santo António dos Capuchos, Lisboa
  • Teresinha Santos Assistente Hospitalar de Medicina Interna, Serviço 1 de Medicina do Hospital de Santo António dos Capuchos, Lisboa
  • A. Barros Veloso Director de Serviço de Medicina Interna, Serviço 1 de Medicina do Hospital de Santo António dos Capuchos, Lisboa

Keywords:

scleroderma renal crisis, secondary hypertension, progressive systemic sclorosis

Abstract

The authors report a case of a 28 year old wo­man, admited to the Hospital by malignant hyper­tension, retinopathy grade IV and intracranial hypertension, associated with poliarthralgia, Raynauds phenomenon, microstomy, scleroda­ ctyly and acute renal failure.

After complete evaluation, we have excluded other causes of secondary hypertension and di­ agnosed progressive systemic sclerosis with mul­tisystem envolvement (kidney, skin, lung, esopha­gus and retine), that had a rare form of presen­tation scleroderma renal crisis (10% of cases) and started emergent antihypertensive treatment with ACE inhibitors (captopril 150 mg daily), ni­fedipine (60 mg daily) and dialysis. We emphazi­se this clinical case because it s a rare disease (2.7 new patients/million/year) that had a rare form of presentation, and had a complete reco­very of renal function after three months of he­ modialysis. She is at the present date with nor­ mal blood pressure without any treatment.

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References

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Additional Files

Published

1996-06-28

How to Cite

1.
Ribeiro da Cunha A, Lourenço J, Santos T, Barros Veloso A. Progressive systemic sclerosis - An unusual presentation. RPMI [Internet]. 1996 Jun. 28 [cited 2024 Nov. 22];3(2):96-100. Available from: https://revista.spmi.pt/index.php/rpmi/article/view/2274

Issue

Vol. 3 No. 2 (1996): Abril/ Junho

Section

Case Reports

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This work is licensed under a Creative Commons Attribution 4.0 International License.

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