Primary Bilateral Adrenal T-Cell Lymphoma: A Case Report
DOI:
https://doi.org/10.24950/rspmi/CC/210/18/3/2019Keywords:
Lymphoma,T-Cell, Adrenal Gland Neoplasms, AutoimmunityAbstract
Primary adrenal lymphoma is an extremely rare entity which
constitutes less than 1% of all extranodal lymphomas. Most
cases are presented with bilateral adrenal masses with or
without extra-adrenal involvement. Presentation may be with
adrenal insufficiency which can be a life-threatening situation. The etiological mechanism is not completely understood but autoimmunity seems to have an important role. We
report a case of a 44-year old man admitted to the Internal
Medicine Department due to thoracic pain, constitutional
symptoms and fever. An abdominal computed tomography
scan revealed bilateral adrenal masses. A left surgical adrenalectomy was performed, and histological examination
diagnosed a non-Hodgkin T-cell lymphoma. Only 5 cases of
T-cell type PAL have been reported in literature. This case
report emphasizes the complexity of differential diagnosis in
the presence of bilateral adrenal masses, the possibility of
lymphoma and the importance of early diagnosis in order to
improve the clinical outcomes. A review of the literature of
this unusual entity was carried out.
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