Angiosarcoma do membro inferior simulando tromboflebite profunda – uma revisão
Palavras-chave:
Angiossarcoma do membro inferior, Linfedema, tromboflebite profundaResumo
Os angiossarcomas são sarcomas com diferenciação vascular,
muito raros, de elevado grau de malignidade. Metastizam precocemente e têm, geralmente, mau prognóstico. O diagnóstico
precoce é importante, de forma a proporcionar cirurgia ablativa
radical, a qual poderá, eventualmente, melhorar o prognóstico.
Os autores apresentam um caso de angiossarcoma da perna
de comportamento muito agressivo, inicialmente diagnosticado
como tromboflebite profunda. A doente foi admitida em fase
avançada de doença, com múltiplas metástases, tendo “exitus”
rápido durante a fase de estudo da situação. Os autores fazem
uma revisão dos angiossarcomas superficiais, incluindo a sua
classificação histopatológica, o seu aspecto multifocal, a precocidade de aparecimento de metástases em vários locais, estudos
diagnósticos necessários para a caracterização de tumores vasculares, recorrências precoces após aparente cirurgia ablativa radical, e opções terapêuticas existentes.
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