Linfoma de Burkitt do cólon direito num jovem adulto

Autores

  • Helena Magalhães Instituto Português de Oncologia Francisco Gentil do Porto, EPE
  • Luís Menezes Falcão Hospital Universitário de Santa Maria

DOI:

https://doi.org/10.24950/rspmi.1017

Palavras-chave:

Linfoma de Burkitt, gene c-myc, vírus Epstein-Barr, regime Hiper-CVAD

Resumo

O linfoma de Burkitt é um linfoma não Hodgkin de células B de
alto grau, pouco comum em adultos, e que compreende três variantes: a endémica, a esporádica e um subgrupo de linfomas
agressivos que ocorre em indivíduos imunodeprimidos.
É o primeiro tumor que se confirmou estar associado a um vírus
(Epstein-Barr) e a translocações cromossómicas, cuja consequência é bem conhecida - desregulação do oncogene c-myc.
Descreve-se o caso de um doente do sexo masculino com 23
anos de idade, raça negra, natural e residente em São Tomé e
Príncipe, com queixas de dor abdominal difusa, massa no flanco
direito, com aumento do volume abdominal e períodos que alternavam entre diarreia e obstipação.
Após a realização de exames complementares foi-lhe diagnosticado linfoma de Burkitt em estádio III, tendo iniciado protocolo
Hiper-CVAD de oito ciclos.

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Publicado

31-12-2014

Como Citar

1.
Magalhães H, Menezes Falcão L. Linfoma de Burkitt do cólon direito num jovem adulto. RPMI [Internet]. 31 de Dezembro de 2014 [citado 24 de Abril de 2024];21(4):149-56. Disponível em: https://revista.spmi.pt/index.php/rpmi/article/view/1017

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