Relapsing angioedema
Keywords:
angioedema, C1 inhibitor deficit, monoclonal gammopathyAbstract
The authors present the case report of a male patient, with a rare and potentially lethal disease, angioedema, due to an acquired deficit of C1 esterase inhibitor, which lead to several emergency room admissions in the two years prior to admission. Additionally, this patient had two extremely rare findings in this type of disease: a normal C1q levai and a monoclonal gammopathy of unknown significance. The authors present a review of the literature of acquired angioedema and the associations with other diseases that are generally found in these patients.
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