Behçet disease and lymphoma. Casual association?
Keywords:
Behçet disease, non-Hodgkin lymphoma, associationAbstract
Behcet disease (BD) is characterized by a triple-symptom complex
of recurrent oral aphthous ulcers, genital ulcers, and uveitis.
Systemic involvement of multiple organs is observed in Behçet
disease, based primarily in the development of vasculitis or
vasculopathies lesions in the affected areas. These areas may
demonstrate microscopic evidence of inflammatory tissue infiltration with both T cells and neutrophils.
Association with Non-Hodgkin Lymphoma has been reported
in few cases, but does not allow establishing causal relationship.
In this paper we report a case of Non-Hodgkin Lymphoma in a
patient with Behçet disease and literature review.
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References
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