Behçet disease in sub-Saharan Africa – a case report

Authors

  • B. Carrilho Serviço de Medicina I do Hospital Universitário de Santa Maria, Lisboa
  • L. Menezes Falcão Serviço de Medicina I do Hospital Universitário de Santa Maria, Lisboa

Keywords:

Behcet disease, sub-Saharan Africa, acute pericard

Abstract

Behcet disease (BD) is a chronic vasculitis that damages many
organic systems. It is considered more prevalent in the areas
surrounding the old silk trading routes in the Middle East and in
Central Asia, being rare in the black race. There are few cases
reported from sub-Saharan Africa. The cardiac involvement is
an unusual clinical manifestation of BD - about 1% -, and acute
pericarditis is one of the most common. We describe a case of a
young black male, from Guinea-Bissau, who presented mucocutaneous lesions, arthritis and precordialgia. A review of the cardiac
involvement in BD is carried out.

Downloads

Download data is not yet available.

References

International Study Group for Behçet’s Disease: Criteria for diagnosis of Behçet’s disease. Lancet 1990; 335:1078.

Moutsopoulos HM. Capítulo 320: Behçet’s Sydrome. In Fauci AS, Braunwald E, Kasper DL, Hauser SL, Longo DL, Jameson JL, Loscalzo J Eds. Harrison’s Principles of Internal Medicine. Nova Iorque: McGraw-Hill, 2008: 2132.

D Buskila, D D Gladman, J Gilmore, and I E Salit: Behçet’s disease in a patient with immunodeficiency virus infection. Ann Rheum Dis. 1991;

(2):115–116.

Jacyk WK. Behçet’s disease in South African blacks: report of five cases. J Am Acad Dermatol 1994; 869:73.

Taylor CB, Low N, Raj S et al. Behçet’s syndrome progressing to gastrointestinal perforation in a West African male. Br J Rheum 1997, 36:498–501.

Dia D, Dieng MT, Sy Ndiaye T et al. Behçet’s disease in Dakar (Senegal): epidemiological and clinical features, Dakar Med. 2003, 48(1):64-67.

Shahram F, Davatchi F, Akbarian M et al. The 1996 survey of Behçet’s disease in Iran, study of 3153 cases. Revue du Rheumatisme 1996; 63: 538.

Gürler A, Boyvat A, Tursen U. Clinical manifestations of Behcet’s disease: an analysis of 2147 patients. Yonsei Med J 1997; 38: 423-427.

Lakhanpal S, Tani K, Lie JT, Katoh K, Ishigatsubo Y, Ohokubo T. Pathologic features of Behçet’s syndrome: a review of Japanese autopsy registry data. Hum Pathol. 1985;16(8):790-795.

Akar et al.; Cardiovascular involvement in Behçet’s disease; Anadolu Kardiyol Derg 2003;3: 261-265.

Morelli et al. Cardiac involvement in Behçet’s disease. Cardiology. 1997;88(6):513-517.

Bertrand Wechsler, Lê Thi Huong Du, Edoardd Kieffer; Manifestations cardio-vasculaires de la maladie de Behçet; Ann Med interne 1999; 150:7.

Atzeni F, Sarzi-Puttini P, Doria A, Boiardi L, Pipitone N, Salvarani C. Behçet’s disease and cardiovascular involvement, Lupus. 2005;14(9):723-726

Additional Files

Published

2010-12-31

How to Cite

1.
Carrilho B, Menezes Falcão L. Behçet disease in sub-Saharan Africa – a case report. RPMI [Internet]. 2010 Dec. 31 [cited 2024 Dec. 18];17(4):241-5. Available from: https://revista.spmi.pt/index.php/rpmi/article/view/1188