Light chain disease

Authors

  • José Carlos Alexandre Assistente Graduado de Medicina Interna, Hospital de São Teotónio, Viseu
  • Miguel R. S. Jorge Silva Internos do Internato Geral, Hospital de São Teotónio, Viseu
  • Edite R. da Costa Internos do Internato Geral, Hospital de São Teotónio, Viseu
  • Maria do Céu Correia Internos do Internato Complementar de Medicina Interna, Hospital de São Teotónio, Viseu
  • Chantal Albuquerque Internos do Internato Complementar de Medicina Interna, Hospital de São Teotónio, Viseu
  • Maria Augusta Cipriano Assistente Graduada de Anatomia Patológica, Hospitais da Universidade de Coimbra
  • Pedro Henriques Chefe de Serviço e Director do Serviço de Medicina I, Hospitais da Universidade de Coimbra

Keywords:

ascites, jaundice, hepatomegaly, light chain disease, plasma cell dyscrasia

Abstract

The authors describe an unusual case of light chain deposition disease in which the clinicai presentation was hepatomegaly, ascites and jaundice, without biochemical evidence of renal involvement.

Light chain disease of the kidney, kappa class, is frequent, and deposition of light chains rarely occur in other organs as the first manifestation of this plasma cell dyscrasia.

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References

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Mignon F, Morel-Maroger L. Cerf M. Preud'Homme JL. & Ri­ chet G. Depots hépatiques et rénaux de chaines légeres kappa révélateurs d 'une dysglobulinémie. Nephrologie 1980: 1: 167-170.

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Additional Files

Published

2000-09-29

How to Cite

1.
Alexandre JC, Jorge Silva MRS, da Costa ER, Correia M do C, Albuquerque C, Cipriano MA, Henriques P. Light chain disease. RPMI [Internet]. 2000 Sep. 29 [cited 2024 May 11];7(3):156-8. Available from: https://revista.spmi.pt/index.php/rpmi/article/view/1996

Issue

Vol. 7 No. 3 (2000): Julho/ Setembro

Section

Case Reports

License

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

Copyright (c) 2023 Medicina Interna

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