Doença de deposição de cadeias leves com atingimento hepático predominante: a propósito de um caso clínico
Palavras-chave:
Doença de depósitos de cadeias levesResumo
A doença de depósitos de cadeias leves (DDCL) é uma das
mais raras discrasias de células plasmocitárias monoclonais.
Caracteriza-se pela infi ltração multissistémica por cadeias leves, sendo o atingimento renal quase universal. O envolvimento
hepático de forma isolada é raro, sendo este órgão geralmente
afectado em doentes que também apresentam doença renal, a
qual normalmente domina o quadro clínico.
Os autores apresentam um caso clínico de DDCL com envolvimento hepático predominante
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Este trabalho encontra-se publicado com a Licença Internacional Creative Commons Atribuição 4.0.
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