Síndroma de Sjögren Primária – revisão

Autores

  • Maria do Céu Coelho Médica do Internato Complementar de Medicina Interna, Hospital de São Teotónio, Viseu
  • Eduardo Melo Assistente de Medicina Interna (UCIP), Hospital de São Teotónio, Viseu
  • Ana Albuquerque Assistente de Medicina Interna (UCIP), Hospital de São Teotónio, Viseu
  • José Pedro Saraiva Assistente Graduado de Anestesiologia (UCIP), Hospital São Teotónio, Viseu
  • António Pimentel Director de Serviço da Unidade de Cuidados Intensivos Polivalente (UCIP), Hospital de São Teotónio, Viseu

Palavras-chave:

Sindroma de Sjögren, xerostomia, xeroftalmia, parotidite, nefrite, pneumonite, tiroide, arterite

Resumo

A síndroma de Sjögren (S.S.) é uma doença inflamatória auto-imune, lentamente
progressiva que, predominantemente, afecta as glândulas exócrinas, clinicamente
dominada pelos sintomas sicca (xerostomia e xeroftalmia), mas que pode, apresentar
quadros clínicos diversos, com sintomas e sinais subtis, de desenvolvimento insidioso, e
por isso, muitas vezes de reconhecimento e diagnóstico difícil.
É considerada por alguns o “grande imitador”, pois pode mimetizar ou coexistir com
outras doenças auto-imunes específicas de órgão, doenças hematológicas ou neurológicas.
Atendendo a estas características, compreender-se-á que , sendo embora uma entidade
comum, seja tão subdiagnosticada e alguns lhe chamem a “doença órfã ”.
Os AA. fazem uma revisão teórica dos aspectos clínicos, histopatológicos,
imunológicos e terapêuticos desta doença.

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Publicado

30-09-2002

Como Citar

1.
Coelho M do C, Melo E, Albuquerque A, Saraiva JP, Pimentel A. Síndroma de Sjögren Primária – revisão . RPMI [Internet]. 30 de Setembro de 2002 [citado 24 de Abril de 2024];9(3). Disponível em: https://revista.spmi.pt/index.php/rpmi/article/view/1861

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