Non-familial systemic amyloidosis

Authors

  • Margarida Ascensão Interna do Internato Complementar de Medicina Interna, Serviços de Medicina II dos Hospitais da Universidade de Coimbra
  • Helena Figueiredo Assistente Hospitalar de Medicina Interna, Serviços de Medicina II dos Hospitais da Universidade de Coimbra
  • José Pontes Assistente Hospitalar de Gastrenterologia, Serviços de Medicina II dos Hospitais da Universidade de Coimbra
  • Ana Paiva Interna do Internato Complementar de Nefrologia, Serviços de Medicina II dos Hospitais da Universidade de Coimbra
  • Paula Pimenta Assistente Hospitalar de Medicina Interna, Serviços de Medicina II dos Hospitais da Universidade de Coimbra
  • Francisco Parente Assistente Hospitalar de Medicina Interna, Serviços de Medicina II dos Hospitais da Universidade de Coimbra
  • José Feio Farmacêutico Hospitalar, Serviços de Medicina II dos Hospitais da Universidade de Coimbra
  • Borges Alexandrino Assistente Graduado de Medicina Interna, Serviços de Medicina II dos Hospitais da Universidade de Coimbra
  • Políbio Serra e Silva Director de Serviço, Serviços de Medicina II dos Hospitais da Universidade de Coimbra

Keywords:

systemic amyloidosis, potassium per­ manganate test, classification, diagnosis, clinical manifestations

Abstract

The authors present the causes of non familial sys­temic amyloidosis seen in a department of Internal Medicine. The work comprises 21 patients with a di­agnosis of amyloidosis. The diagnostic distribution varied between primary (AL), secondary (AA) and b -microglobuün (b2m). The study group was comprised­ of 13 on women (62%) and 8 men (38%) with an average age of 61.5 years ( min. 31/max. 85).

ln this group the authors studied some aspects wich highlight the causes that lead to the investigation of amyloidosis, the associated pathologies, the clinical­ laboratorial syndromes the distribution of the seve­ral types of amyloidosis, the biopsy locations, the evo­lution of the diseases and the patients survivaL

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Additional Files

Published

1997-09-30

How to Cite

1.
Ascensão M, Figueiredo H, Pontes J, Paiva A, Pimenta P, Parente F, Feio J, Alexandrino B, Serra e Silva P. Non-familial systemic amyloidosis. RPMI [Internet]. 1997 Sep. 30 [cited 2025 Apr. 24];4(3):156-62. Available from: https://revista.spmi.pt/index.php/rpmi/article/view/2225

Issue

Vol. 4 No. 3 (1997): Julho/ Setembro

Section

Original Articles

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