Secondary amylodosis AA with P component
Keywords:
secondary amyloidosis AA with P component, nephrotic syndrome, congestive heart failureAbstract
The authors report a case of a 69 years old patient with a history of chronic obstructive lung disease and tuberculosis. ln February 1994 he was admited with refractory congestive heart failure and chronic respiratory failure. One month after discharge, the patient was readmited with anasarca secondary to nephrotic syndrome. Renal biopsy revealed amyloidosis AA with P component. Heredofamiliar amyloidosis and other causes of secondary amyloidosis were excluded. Final diagnosis was amyloidosis secondary to chronic respiratory infections and tuberculosis. Eight weeks after admission acute renal failure developed and hemodialysis was started. The patient died 6 weeks later. At necropsy amyloidosis was confirmed with envolvement of the kidney and vessels of myocardium, lung, adrenal gland and skin. The imunocitochemical test revealed secondary amyloidosis.
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