Splenic hamartoma with haematologic disorders

Authors

  • J. Bernardes Correia Assistente Hospitalar de Medicina Interna, Hospitais da Universidade de Coimbra
  • Benilde Barbosa Interna do Internato Complementar de Medicina lnterna, Hospitais da Universidade de Coimbra
  • Bruno Rodrigues Interno do Internato Complementar de Neurologia, Hospitais Universidade de Coimbra
  • Henrique Ferrão Assistente Hospitalar de Cirurgia Geral, Hospitais Universidade de Coimbra
  • João Correia Assistente Hospitalar de Medicina Interna, Hospital da Guarda
  • Fernando Martinho Director do Serviço de Cirurgia II, Hospitais Universidade de Coimbra
  • Fernando Santos Chefe de Serviço de Medicina Interna dos Hospitais da Universidade de Coim­bra
  • Maria Helena Saldanha Directora do Serviço de Medicina I, Hospitais da Universidade de Coimbra

Keywords:

splenic hamartoma, haematologic disorders

Abstract

Hamartomas of the spleen are rare benign tumour­ like lesions composed mainly of vascular elements. Most of them, remain small in size and asymptomatic, and are therefore, incidental findings at laparotomy or autopsy. However, occasionally, they present with symptoms among wich, haematologic disorders appear in a very few cases.

The authors report a case of splenic hamartoma in a 44-year-old woman with pancytopenia. Prolonged enhancement on post-contrast CT and MR imaging was a useful finding in differentiation of splenic hamartoma from malignant lesions of the spleen. Hamartomas should be kept in mind in the differential diagnosis of splenic tumors. Splenectomy, is indicated in cases where malignancy cannot be excluded and in cases of associated haematologic disorders. The haematologic abnormalities, disapeared after removal of the spleen.

By review of the literature, they are less than two tens of well-documented cases of symptomatic splenic hamartomas associated with haematologic disorders.

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Additional Files

Published

1999-03-31

How to Cite

1.
Bernardes Correia J, Barbosa B, Rodrigues B, Ferrão H, Correia J, Martinho F, Santos F, Saldanha MH. Splenic hamartoma with haematologic disorders. RPMI [Internet]. 1999 Mar. 31 [cited 2024 May 11];6(1):50-3. Available from: https://revista.spmi.pt/index.php/rpmi/article/view/2040

Issue

Vol. 6 No. 1 (1999): Janeiro/ Março

Section

Case Reports

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