O Guerreiro Capestrano em Portugal Doença de Madelung: casos clínicos e revisão da literatura
Palavras-chave:
Doença Madelung, lipomatose simétrica benigna, síndrome Lanois-Bensaude, alcoolismo crónicoResumo
A doença de Madelung é uma patologia rara de etiologia desconhecida, caracterizada pelo desenvolvimento progressivo de
tecido adiposo subcutâneo não capsulado a nível do pescoço,
ombros, braços e tronco. Apesar de benigno, o envolvimento do
pescoço e do mediastino pode causar síndromes compressivos
da traqueia e da veia cava superior condicionando dispneia,
disfagia e disfonia. Afecta predominantemente homens, com
idade compreendida entre os 30 e os 60 anos, de origem mediterrânica e com antecedentes de hábitos alcoólicos. Pode estar
associada a hiperlipoproteinemia, hiperuricemia, diabetes mellitus
e hipotiroidismo. O único tratamento eficaz é a lipectomia ou a
lipoaspiração, mas a recorrência é comum. São apresentados
dois casos clínicos de doentes do sexo masculino com aparência
pseudoatlética e história de consumo excessivo de álcool.
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Referências
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