Two cases of dermatomyositis: so equal and so different
Keywords:
Dermatomyositis, inflammatory myopathys, neoplasiaAbstract
Dermatomyositis is a rare systemic autoimmune disease, which
usually presents with muscular weakness and typical rash. With
adequate treatment 90% of the patients are alive 5 years after
the diagnosis. However, in one group of these patients, dermatomyositis is part of a paraneoplasic syndrome and, in this one,
the treatment response decreases and the prognosis is worse.
The authors present clinical cases of two 68 year old men,
with muscular weakness, dysphagia and typical rash, but with
different treatment response and clinical results which mirrored
the influence of an associated neoplastic disease on the course
of dermatomyositis.
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