Light chain deposition disease with predominant hepatic involvement – a clinical case report
Keywords:
Lightchain deposition diseaseAbstract
Light chain deposition disease (LCDD) is one of the least common
of the monoclonal plasma cell dyscrasias. It is characterized by
multi-systemic infi ltrative light chains, with the kidney being
almost always involved. Isolated liver involvement is rare and this
organ is usually affected in patients who also have renal disease,
dysfunction of which is the commonest clinical presentation. The
authors report a patient who presented LCDD with predominantly
hepatic involvement.
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