Haemophagocytic syndrome and Still’s Disease in the Adult
Keywords:
Adult Still´s disease, hyperferritinaemia, haemophagocytic syndromeAbstract
Adult Still’s disease is a rare disease found worlwide. It presents
as an acute febrile syndrome that affects multiple organs. Although
the diagnosis is one of exclusion, a striking constellation of clinical
and laboratory abnormalities is present.
The authors report a case of Adult Still´s Disease in a 58-year- s Disease in a 58-year old woman who presented with fever, arthralgia, sore throat, rash and myalgia and elevated serum ferritin. Although the patient
initially responded favourably to corticotherapy, the outcome was
fatal. The authors discuss the macrophage activation syndrome
as a complication of chronic rheumatic diseases and as a consequence of Parvovirus infection.
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