Isolated noncompaction of myocardium in adults

Authors

  • Jorge Nunes Hospital de Curry Cabral, Lisbon, Portugal
  • Sandra Bráz Hospital de Curry Cabral, Lisbon, Portugal
  • Aline Gonçalves Hospital de Curry Cabral, Lisbon, Portugal
  • Conceição Loureiro Hospital de Curry Cabral, Lisbon, Portugal
  • Ana Galrinho Hospital de Curry Cabral, Lisbon, Portugal
  • Conceição Pernadas Hospital de Curry Cabral, Lisbon, Portugal
  • António Murinello Hospital de Curry Cabral, Lisbon, Portugal

Keywords:

Noncompaction, echocardiography, spongy myocardium

Abstract

Isolated noncompaction of ventricular myocardium, or spongy myocardium, is a rare form
of congenital cardiomyopathy, characterized by the presence of prominent trabeculations and
deep intertrabecular recesses which communicate with the ventricular cavity. Heart failure,
ventricular arrhythmias and systemic embolism are the major clinical manifestations. Although this is a congenital disorder, onset of symptoms can occur late in adults. The authors present a case of late diagnosis: a 62-year-old male, in which image evaluation showed the pathognomonic features of the disease.

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References

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Additional Files

Published

2004-03-31

How to Cite

1.
Nunes J, Bráz S, Gonçalves A, Loureiro C, Galrinho A, Pernadas C, Murinello A. Isolated noncompaction of myocardium in adults . RPMI [Internet]. 2004 Mar. 31 [cited 2024 Dec. 18];11(1):23-6. Available from: https://revista.spmi.pt/index.php/rpmi/article/view/1724

Issue

Vol. 11 No. 1 (2004): Janeiro/ Março

Section

Case Reports

License

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This work is licensed under a Creative Commons Attribution 4.0 International License.

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