Wegener Granulomatosis

Authors

  • Cristina João Interna do Complementar de Oncologia, UCIP
  • Elizabet Santos Interna do Complementar de Oncologia, Serviço de Medicina II, Hospital Fernando da Fonseca, Amadora
  • Alfredo Leite Assistente Hospitalar de Medicina Interna, UCIP
  • Cristina Miranda Assistente Hospitalar de Medicina Interna, UCIP
  • Isabel Serra Assistente Hospitalar de Medicina Interna, UCIP, Hospital Fernando da Fonseca, Amadora
  • Luís Revés Assistente Hospitalar de Medicina Interna, UCIP, Hospital Fernando da Fonseca, Amadora
  • Teresa Brandão Consultora de Medicina Interna, UCIP, Hospital Fernando da Fonseca, Amadora
  • Fernanda Martins Assistente Graduado de Medicina Interna, – Serviço de Medicina II, Hospital Fernando da Fonseca, Amadora
  • Paulo Freitas Director de Serviço, UCIP, Hospital Fernando da Fonseca, Amadora
  • Luis Dutschmann Director de Serviço, Serviço de Medicina II, Hospital Fernando da Fonseca, Amadora

Keywords:

Wegener granulomatosis, dyspnea, lung-kidney syndrome

Abstract

Wegener’s granulomatosis is a systemic vasculitis
of the small and median vessels, with particular
involvement of the upper and lower respiratory tracts
and the kidney. This distinct clinico-pathologic entity
is included in the differential diagnosis of lung-kidney syndrome.
The authors present the clinical case of a 59 year old woman, admitted to the Polyvalent Intensive Care
Unit of Fernando da Fonseca Hospital, with haemoptysis and respiratory and renal insufficiency.
The aetiologic investigation is described and a
diagnosis of Wegener’s granulomatosis was made.
The authors discuss relevant aspects of the
diagnosis, therapeutics and follow-up of patients with this disease.

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References

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Additional Files

Published

2001-09-28

How to Cite

1.
João C, Santos E, Leite A, Miranda C, Serra I, Revés L, Brandão T, Martins F, Freitas P, Dutschmann L. Wegener Granulomatosis. RPMI [Internet]. 2001 Sep. 28 [cited 2024 Dec. 18];8(3):150-3. Available from: https://revista.spmi.pt/index.php/rpmi/article/view/1911

Issue

Vol. 8 No. 3 (2001): Julho/ Setembro

Section

Case Reports

License

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This work is licensed under a Creative Commons Attribution 4.0 International License.

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